E71 Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
Non-billable header ICD10CM Release FY2026
Short description: Disord of branched-chain amino-acid metab & fatty-acid metab
Version history
| Release | Valid from | Valid to | Description | Billable |
|---|---|---|---|---|
| FY2026 | 2025-10-01 | current | Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism | no |
Related codes in E71
- E71.0 Maple-syrup-urine disease
- E71.1 Other disorders of branched-chain amino-acid metabolism
- E71.11 Branched-chain organic acidurias
- E71.110 Isovaleric acidemia
- E71.111 3-methylglutaconic aciduria
- E71.118 Other branched-chain organic acidurias
- E71.12 Disorders of propionate metabolism
- E71.120 Methylmalonic acidemia
- E71.121 Propionic acidemia
- E71.128 Other disorders of propionate metabolism
- E71.19 Other disorders of branched-chain amino-acid metabolism
- E71.2 Disorder of branched-chain amino-acid metabolism, unspecified
- E71.3 Disorders of fatty-acid metabolism
- E71.30 Disorder of fatty-acid metabolism, unspecified
- E71.31 Disorders of fatty-acid oxidation
- E71.310 Long chain/very long chain acyl CoA dehydrogenase deficiency
- E71.311 Medium chain acyl CoA dehydrogenase deficiency
- E71.312 Short chain acyl CoA dehydrogenase deficiency
- E71.313 Glutaric aciduria type II
- E71.314 Muscle carnitine palmitoyltransferase deficiency