E71 — ICD-10-CM Diagnosis Codes

• E71 Disorders of branched-chain amino-acid metabolism and fatty-acid metabolism
• E71.0 Maple-syrup-urine disease billable
• E71.1 Other disorders of branched-chain amino-acid metabolism
• E71.11 Branched-chain organic acidurias
• E71.110 Isovaleric acidemia billable
• E71.111 3-methylglutaconic aciduria billable
• E71.118 Other branched-chain organic acidurias billable
• E71.12 Disorders of propionate metabolism
• E71.120 Methylmalonic acidemia billable
• E71.121 Propionic acidemia billable
• E71.128 Other disorders of propionate metabolism billable
• E71.19 Other disorders of branched-chain amino-acid metabolism billable
• E71.2 Disorder of branched-chain amino-acid metabolism, unspecified billable
• E71.3 Disorders of fatty-acid metabolism
• E71.30 Disorder of fatty-acid metabolism, unspecified billable
• E71.31 Disorders of fatty-acid oxidation
• E71.310 Long chain/very long chain acyl CoA dehydrogenase deficiency billable
• E71.311 Medium chain acyl CoA dehydrogenase deficiency billable
• E71.312 Short chain acyl CoA dehydrogenase deficiency billable
• E71.313 Glutaric aciduria type II billable
• E71.314 Muscle carnitine palmitoyltransferase deficiency billable
• E71.318 Other disorders of fatty-acid oxidation billable
• E71.32 Disorders of ketone metabolism billable
• E71.39 Other disorders of fatty-acid metabolism billable
• E71.4 Disorders of carnitine metabolism
• E71.40 Disorder of carnitine metabolism, unspecified billable
• E71.41 Primary carnitine deficiency billable
• E71.42 Carnitine deficiency due to inborn errors of metabolism billable
• E71.43 Iatrogenic carnitine deficiency billable
• E71.44 Other secondary carnitine deficiency
• E71.440 Ruvalcaba-Myhre-Smith syndrome billable
• E71.448 Other secondary carnitine deficiency billable
• E71.5 Peroxisomal disorders
• E71.50 Peroxisomal disorder, unspecified billable
• E71.51 Disorders of peroxisome biogenesis
• E71.510 Zellweger syndrome billable
• E71.511 Neonatal adrenoleukodystrophy billable
• E71.518 Other disorders of peroxisome biogenesis billable
• E71.52 X-linked adrenoleukodystrophy
• E71.520 Childhood cerebral X-linked adrenoleukodystrophy billable
• E71.521 Adolescent X-linked adrenoleukodystrophy billable
• E71.522 Adrenomyeloneuropathy billable
• E71.528 Other X-linked adrenoleukodystrophy billable
• E71.529 X-linked adrenoleukodystrophy, unspecified type billable
• E71.53 Other group 2 peroxisomal disorders billable
• E71.54 Other peroxisomal disorders
• E71.540 Rhizomelic chondrodysplasia punctata billable
• E71.541 Zellweger-like syndrome billable
• E71.542 Other group 3 peroxisomal disorders billable
• E71.548 Other peroxisomal disorders billable